Desmoplastic small round cell tumor of the pleura

Last revised by Sally Ayesa on 30 Apr 2022

Citation, DOI, disclosures and article data

Citation:

Weerakkody Y, Ayesa S, Desmoplastic small round cell tumor of the pleura. Reference article, Radiopaedia.org (Accessed on 25 Apr 2024) https://doi.org/10.53347/rID-99418

DOI:

https://doi.org/10.53347/rID-99418

Permalink:

https://radiopaedia.org/articles/99418

rID:

99418

Article created:

29 Apr 2022, Yuranga Weerakkody ◉

Disclosures:

At the time the article was created Yuranga Weerakkody had no recorded disclosures.

View Yuranga Weerakkody's current disclosures

Last revised:

30 Apr 2022, Sally Ayesa ◉

Disclosures:

At the time the article was last revised Sally Ayesa had no recorded disclosures.

View Sally Ayesa's current disclosures

Revisions:

2 times, by 2 contributors - see full revision history and disclosures

Systems:

Chest

Synonyms:

Desmoplastic round cell tumour of pleura
DSRTC pleura
Desmoplastic small round cell tumour of pleura
Pleural DSRTC

Desmoplastic small round cell tumor (DSRCT) of the pleura is a rare primary pleural malignancy comprising of mesenchymal cells.

Epidemiology

Tend to occur in younger patients (mean ~ 25.5 years) and with a slightly greater male predilection.

Treatment and prognosis

DSRCT tend to be aggressive tumors with a poor prognosis.

History and etymology

DSRCT was first described in 1989 by Gerald and Rosai and Ordonez et al. as a highly aggressive and rare mesenchymal tumor arising from serosal surfaces.