Adenoid cystic carcinoma
An adenoid cystic carcinoma (ACC) refers to a rare histological sub-type of adenocarcinoma. It is generally considered low grade 4. The tumors have wide distribution and mainly occur in relation to the airways, lacrimal glands and breast. The tumors have notable tendency for perineural extension.
Clinical presentation and radiographic features are best discussed according to individual locations.
Reported locations include
- head and neck
- breast - adenoid cystic carcinoma of breast 2
- tracheo-bronchial tree / respiratory tract
adenoid cystic carcinoma of tracheo bronchial tree
- 2nd most common malignant primary tracheal neoplasm (after squamous cell carcinoma) 4
- also previously called a cylindroma in this location 4
- adenoid cystic carcinoma of the lungs
- adenoid cystic carcinoma of tracheo bronchial tree
- uterine and cervical
- Bartholin glands - adenoid cystic carcinoma of Bartholin glands