Cochlear incomplete partition is a group of cochlear malformations associated with variable other inner ear architecture defects. These malformations have in common that the cochlea is clearly separated from the vestibule and the external contour of the cochlea is nearly normal in size, but there are defects involving the modiolus and interscalar septa 1,2.
According to the CT-based classification that Sennaroglu proposed in 2002 and subsequently revised 2,3, there are three types of incomplete partition:
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cochlear incomplete partition type I (IP-I)
- also known as cystic cochleovestibular malformation
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cochlear incomplete partition type II (IP-II)
- when associated with enlarged vestibule aqueduct and mildly dilated vestibule, the triad is known as Mondini malformation
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cochlear incomplete partition type III (IP-III)
- observed in X-linked deafness