Hepatoblastoma (staging)

Last revised by Mohamed Saber on 28 Oct 2020

Citation, DOI, disclosures and article data

Citation:

Gaillard F, Saber M, Knipe H, et al. Hepatoblastoma (staging). Reference article, Radiopaedia.org (Accessed on 18 Apr 2024) https://doi.org/10.53347/rID-8405

DOI:

https://doi.org/10.53347/rID-8405

Permalink:

https://radiopaedia.org/articles/8405

rID:

8405

Article created:

28 Jan 2010, Frank Gaillard ◉ ◈

Disclosures:

At the time the article was created Frank Gaillard had no recorded disclosures.

View Frank Gaillard's current disclosures

Last revised:

28 Oct 2020, Mohamed Saber ◉

Disclosures:

At the time the article was last revised Mohamed Saber had no recorded disclosures.

View Mohamed Saber's current disclosures

Revisions:

3 times, by 3 contributors - see full revision history and disclosures

Systems:

Hepatobiliary, Paediatrics, Oncology

Sections:

Staging

Tags:

cases, refs

As expected there are a number of different staging systems for hepatoblastoma.

Staging

PRETEXT grouping system of pediatric liver tumors
- not specific to hepatoblastoma; used in all pediatric liver tumors
Intergroup staging system
- specific for hepatoblastoma (see below)

Intergroup staging system

stage I
- complete surgical resection
stage II
- IIa
  - complete macroscopic surgical resection
  - intrahepatic residual microscopic disease
- IIb
  - complete macroscopic surgical resection
  - extrahepatic residual microscopic disease
stage III
- IIIa
  - incomplete surgical resection with macroscopic residual AND / OR
  - significant tumor spill AND / OR
  - positive lymph node disease
- IIIb
  - tumor not resected
stage IV
- IVa
  - distant metastatic disease
  - primary tumor completely resected
- IVb
  - distant metastatic disease
  - primary tumor incompletely resected