Interstitial lung disease associated with primary biliary cholangitis

Last revised by David Luong on 5 Feb 2022

Citation, DOI, disclosures and article data

Citation:

Weerakkody Y, Luong D, Bell D, Interstitial lung disease associated with primary biliary cholangitis. Reference article, Radiopaedia.org (Accessed on 24 Apr 2024) https://doi.org/10.53347/rID-94748

DOI:

https://doi.org/10.53347/rID-94748

Permalink:

https://radiopaedia.org/articles/94748

rID:

94748

Article created:

14 Nov 2021, Yuranga Weerakkody ◉

Disclosures:

At the time the article was created Yuranga Weerakkody had no recorded disclosures.

View Yuranga Weerakkody's current disclosures

Last revised:

5 Feb 2022, David Luong ◉

Disclosures:

At the time the article was last revised David Luong had no recorded disclosures.

View David Luong's current disclosures

Revisions:

4 times, by 3 contributors - see full revision history and disclosures

Systems:

Chest, Hepatobiliary

Synonyms:

Interstitial lung disease associated with primary biliary cirrhosis
ILD in PBC

Interstitial lung disease associated with primary biliary cholangitis can occur in a variable pattern that can include ¹:

Epidemiology

It may occur in approximately 15% of patients with primary biliary cholangitis².

There may be a higher predilection in older patients and in those with an elevated erythrocyte sedimentation rate (ESR). Concomitant presence of Sjögren syndrome can considerably increase the risk of interstitial lung disease.