Intraconal orbital lesions are broadly divided into two main groups; those with or without involvement of the optic nerves.
Lesions with optic nerve involvement:
- optic nerve glioma
- optic nerve meningioma
- optic neuritis
- pseudotumor
- lymphoma and leukemia
- intracranial hypertension
- retinoblastoma
Lesions without optic nerve involvement:
- cavernous hemangioma: also known as slow flow venous malformation; most common orbital vascular lesion, usually in lateral intraconal space
- capillary hemangioma
- orbital varix
- arteriovenous malformation
- retro-orbital hematoma
- lymphangioma
- schwannoma
- sarcoidosis
- Erdheim-Chester Disease
- coloboma
- metastasis: breast cancer, melanoma, etc.
- melanoma: primary or metastasis