Citation, DOI, disclosures and article data
Citation:
Weerakkody Y, Tatco V, Jones J, Mixed connective tissue disease (pulmonary manifestations). Reference article, Radiopaedia.org (Accessed on 28 Mar 2024) https://doi.org/10.53347/rID-24595
Pulmonary manifestations of mixed connective tissue disease can be seen in a wide range (20-85%) of those of mixed connective tissue disease. It can have multiple manifestations.
More commonly described features include:
Other rare presentations include:
Individual imaging features are nonspecific on their own.
A prerequisite for the diagnosis of mixed connective tissue disease is the presence, in the serum, of high titers of antibodies against uridine-rich RNA-small nuclear ribonucleoprotein (snRNP) 2.
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