Ossifying renal tumor of infancy (ORTI) is a rare renal tumor.
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Epidemiology
- extremely rare, <<1% of pediatric renal neoplasms (17 cases reported)
- 6 days - 3 months
- male predominant
Pathology
Histology reveals spindle cells and osteoblastic cells in a calcified osteoid matrix. It is thought to originate from intralobar nephrogenic rests.
Radiographic features
Abdominal radiography
- often resembles a staghorn calculus
Ultrasound
- calcification is hyperechoic
- there may be intra-tumoral flow on color Doppler ultrasound
CT
ORTI may resemble a staghorn calculus since it originates from the renal papilla, but it enhances postcontrast.
Treatment and prognosis
Cases of ORTI so far have been benign, with no recurrence after resection.
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