Pancreatic mesenchymal neoplasms
Updates to Article Attributes
Pancreatic mesenchymal neoplasms (or pancreatic nonepithelial neoplasms) are a group of rare pancreatic neoplasms that arise from the structural elements of the pancreas (nerves, fat, lymph), rather than from the exocrine or endocrine cells of the pancreas. Neoplasms from exocrine and endocrine cells result in more familiar pancreatic neoplasms such as pancreatic ductal adenocarcinoma, IPMN, and pancreatic endocrine tumors (formerly termed "islet cell tumors").
Epidemiology
Pancreatic mesenchymal neoplasms are rare and represent at most 1-2% of pancreatic neoplasms 2.
Pathology
Pancreatic nonepithelial tumorstumours include
Benign
- pancreatic neurofibroma
- pancreatic schwannoma
- pancreatic ganglioneuroma
- pancreatic desmoid
tumortumour - pancreatic lipoma
-
pancreatic perivascular epithelioid cell
tumor (PEComatumour (PEComa) - pancreatic mature cystic teratoma (dermoid)
- pancreatic lymphangioma
Malignant
Radiographic features
A disparate group of tumors, they have different imaging appearances, based on their underlying histology. As a group, these neoplasms tend to better-marginated than the more infiltrative pancreatic ductal adenocarcinoma 1.
-<p><strong>Pancreatic mesenchymal neoplasms</strong> (or <strong>pancreatic nonepithelial neoplasms</strong>) are a group of rare <a href="/articles/pancreatic-neoplasms">pancreatic neoplasms</a> that arise from the structural elements of the pancreas (nerves, fat, lymph), rather than from the exocrine or endocrine cells of the pancreas. Neoplasms from exocrine and endocrine cells result in more familiar pancreatic neoplasms such as <a href="/articles/pancreatic-ductal-carcinoma">pancreatic ductal adenocarcinoma</a>, <a href="/articles/intraductal-papillary-mucinous-neoplasm">IPMN</a>, and <a href="/articles/endocrine-tumours-of-the-pancreas">pancreatic endocrine tumors</a> (formerly termed "islet cell tumors").</p><h4>Epidemiology</h4><p>Pancreatic mesenchymal neoplasms are rare and represent at most 1-2% of pancreatic neoplasms <sup>2</sup>.</p><h4>Pathology</h4><p>Pancreatic nonepithelial tumors include</p><h5>Benign</h5><ul>- +<p><strong>Pancreatic mesenchymal neoplasms</strong> (or <strong>pancreatic nonepithelial neoplasms</strong>) are a group of rare <a href="/articles/pancreatic-neoplasms">pancreatic neoplasms</a> that arise from the structural elements of the pancreas (nerves, fat, lymph), rather than from the exocrine or endocrine cells of the pancreas. Neoplasms from exocrine and endocrine cells result in more familiar pancreatic neoplasms such as <a href="/articles/pancreatic-ductal-carcinoma">pancreatic ductal adenocarcinoma</a>, <a href="/articles/intraductal-papillary-mucinous-neoplasm">IPMN</a>, and <a href="/articles/endocrine-tumours-of-the-pancreas">pancreatic endocrine tumors</a> (formerly termed "islet cell tumors").</p><h4>Epidemiology</h4><p>Pancreatic mesenchymal neoplasms are rare and represent at most 1-2% of pancreatic neoplasms <sup>2</sup>.</p><h4>Pathology</h4><p>Pancreatic nonepithelial tumours include</p><h5>Benign</h5><ul>
-<li><a href="/articles/missing">pancreatic desmoid tumor</a></li>- +<li><a href="/articles/missing">pancreatic desmoid tumour</a></li>
-<li>pancreatic perivascular epithelioid cell tumor (PEComa)</li>-<li>pancreatic mature cystic teratoma (dermoid)</li>- +<li>
- +<a title="pancreatic perivascular epithelioid cell tumour" href="/articles/pancreatic-perivascular-epithelioid-cell-tumour">pancreatic perivascular epithelioid cell tumour</a> (<a title="PEComa" href="/articles/pecoma">PEComa</a>)</li>
- +<li>
- +<a title="pancreatic mature cystic teratoma" href="/articles/pancreatic-mature-cystic-teratoma">pancreatic mature cystic teratoma</a> (dermoid)</li>
-<li>pancreatic sarcoma</li>- +<li><a title="pancreatic sarcoma" href="/articles/pancreatic-sarcoma">pancreatic sarcoma</a></li>
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