Primary intracranial leiomyosarcomas are primary malignant tumors derived from smooth muscle cell lineage in the cranial vault.
Primary intracranial leiomyosarcomas are extremely rare. Most commonly, these lesions have been described as EBV-associated smooth muscle tumors in patients who are immunocompromised due to HIV infection.
Intracranial leiomyosarcoma usually appears as an extra-axial mass 1,2, with intra-axial mass being a rare presentation 3,4.
The signal characteristics are non-specific 4.
- isointense to hypointense
- vividly enhancing and heterogeneous
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