Ramsay Hunt syndrome classically presents with a triad of 3,4:
- otic pain
- facial nerve palsy
- a vesicular eruption (often painful) involving the external auditory canal, pinna, tongue or hard palate
The syndrome is due to latent infection of the geniculate ganglion with varicella zoster virus and subsequent reactivation.
Imaging is identical to that seen in Bell palsy, with increased enhancement of the facial nerve. Care should be taken not to mistake normal facial nerve enhancement on MRI for that observed in Ramsay Hunt syndrome.
History and etymology
This eponymous syndrome was named after James Ramsay Hunt, an American neurologist (1872-1937) 2.
- 1. Swartz J, Harnsberger H. Imaging of the temporal bone. Georg Thieme Verlag. ISBN:0865777004. Read it at Google Books - Find it at Amazon
- 2. Louis ED, Williams M. A biography of James Ramsay Hunt (1874-1937). (2003) Journal of the history of the neurosciences. 12 (3): 266-75. doi:10.1076/jhin.12.3.266.16672 - Pubmed
- 3. Monsanto RD, Bittencourt AG, Bobato Neto NJ, Beilke SC, Lorenzetti FT, Salomone R. Treatment and Prognosis of Facial Palsy on Ramsay Hunt Syndrome: Results Based on a Review of the Literature. (2016) International archives of otorhinolaryngology. 20 (4): 394-400. doi:10.1055/s-0036-1584267 - Pubmed
- 4. Robillard RB, Hilsinger RL, Adour KK. Ramsay Hunt facial paralysis: clinical analyses of 185 patients. (1986) Otolaryngology--head and neck surgery : official journal of American Academy of Otolaryngology-Head and Neck Surgery. 95 (3 Pt 1): 292-7. doi:10.1177/01945998860953P105 - Pubmed