Ribbon ribs deformity
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Ribbon-ribs deformity refers to the presence of thinned ribs on image studies. Such finding could be present in patients with Neurofibromatosis type 1 (NF1) due the presence of multiple neurofibromas of intercostal nerves.
This deformity is also described in osteogenesis imperfecta, Edwards syndrome (trisomy 18), and Gorham’s disease.
-<p><strong>Ribbon-ribs deformity</strong> refers to the presence of thinned ribs on image studies. Such finding could be present in patients with <a title="Neurofibromatosis type 1 (NF1)" href="/articles/neurofibromatosis-type-1">Neurofibromatosis type 1 (NF1)</a> due the presence of multiple neurofibromas of intercostal nerves. </p><p>This deformity is also described in <a title="Osteogenesis Imperfecta" href="/articles/osteogenesis-imperfecta-1">osteogenesis imperfecta</a>, <a title="Edward syndrome" href="/articles/edward-syndrome">Edwards syndrome</a> (trisomy 18), and <a title="Gorham disease" href="/articles/gorham-disease">Gorham’s disease</a>.</p>- +<p><strong>Ribbon-ribs deformity</strong> refers to the presence of thinned ribs on image studies. Such finding could be present in patients with <a href="/articles/neurofibromatosis-type-1">Neurofibromatosis type 1 (NF1)</a> due the presence of multiple neurofibromas of intercostal nerves. </p><p>This deformity is also described in <a href="/articles/osteogenesis-imperfecta-1">osteogenesis imperfecta</a>, <a href="/articles/edwards-syndrome-1">Edwards syndrome</a> (trisomy 18), and <a href="/articles/gorham-disease">Gorham’s disease</a>.</p>
Sections changed:
- Signs
Systems changed:
- Musculoskeletal
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- refs
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