Presentation
One week history of left-sided weakness.
Patient Data
Age: 3 years
Gender: Female
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The supraclinoid ICA and P1 segments of the PCA are occluded with large perforator collaterals. A number of basal ganglia infarcts are noted on DWI.
From the case:
Moyamoya disease
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Angiogram confirms extensive perforator colaterals giving the 'puff of smoke' characteristic of this disease, and involving both anterior and posterior circulation.
Case Discussion
Typical features of moya moya disease in the typical age group, and presenting in the typical fashion for this age group - namely infarcts.