Presentation
Long standing progressive shortness of breath
Patient Data
Chest x-ray demonstrates extensive increase in interstitial markings with distortion of the underlying parenchymal architecture. When compared to previous imaging (not shown) these findings are long-standing.
CT of the chest confirms extensive changes of pulmonary fibrosis, most marked in the bases and peripherally. The pulmonary arteries centrally are prominent suggesting a degree of pulmonary arterial hypertension.
Case Discussion
This elderly patient has had well documented long-standing idiopathic pulmonary fibrosis for many years, and is progressively becoming shorter of breath, likely due to a combination of restrictive pulmonary disease, decreased gas exchange and pulmonary arterial hypertension.