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Moyamoya pattern

Case contributed by Frank Gaillard
Diagnosis certain

Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.

dsa

DSA vertebrobasilar system: note the occluded posterior cerebral arteries bilaterally.

DSA  right ICA: markedly stenosed distal Rt ICA with neovascular tufts. 

DSA left ICA: occluded left ICA.

mri

Bilateral watershed infarcts

Case Discussion

Moyamoya disease is a vasculo-occlusive disease involving the circle of Willis, typically the terminal ICA. 

The term moyamoya disease should be reserved for an idiopathic, sometimes familial, condition, which leads to characteristic intracranial vascular changes. Numerous entities have been described which mimic the appearance, in which case the term moyamoya phenomenon, syndrome or pattern is used. 

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