Zinner syndrome

Discussion:

A case of Zinner syndrome with an ectopic insertion of the right ureter into the dilated vas deferens.

Key points of this syndrome:

  • is a triad of Mullerian duct anomalies comprising unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ejaculatory duct obstruction

  • typically diagnosed at 3rd or 4th decade of life

  • occurs due to maldevelopment of the distal part of the mesonephric duct which results in atresia of the ejaculatory duct (leading to obstruction and dilatation of the seminal vesicle) and abnormal ureteral budding (leads to renal agenesis/dysplasia)

An additional finding in this case:

  • high T1W signal intensity within the dilated ducts is probably due to high proteinaceous content as a result of stasis

    Create a new playlist
Loading...