Known congenital heart disease, although no intervention was supposedly done when young. Dyspnea on exertion. 2D echocardiography showed a ventricular septal defect, severe mitral regurgitation and mild to moderate pulmonary regurgitation. She was referred to a tertiary medical center for further evaluation.

CT for the evaluation of interrupted aortic arch (IAA) is essential during presurgical planning, detection of associated cardiac anomalies, determination of the size of the patent ductus arteriosus, and presence of stenosis. CT also detects the presence of vascular collaterals such as in this patient, which allows for some individuals to survive to adulthood without surgical intervention. 90% of infants with interrupted aortic arches usually die within the first year of life from circulatory failure.

An interrupted aortic arch (IAA) type A (Celoria-Patton classification) is the second most common type (approximately 42% of all IAA cases), with type B the most common. This type A arch occurs when the interruption occurs beyond the left subclavian artery. The subclavian arteries of this patient are normal in configuration, without aberrant origin; hence, this may be further subdivided to subtype 1 (normal subclavian artery). The specific types and subtypes are further discussed in the main article regarding interrupted aortic arches.