Retinoblastoma - advanced

Discussion:

Retinoblastoma is the commonest ocular malignancy in childhood, occuring chiefly in those under 4 years of age.  This is a case of a retinoblatoma with intraorbital and intracranial extension along the optic nerve and optic chiasma with a contiguous suprasellar mass and resultant hydrocephalus in keeping with stage IV disease.

Stage IV: metastatic disease

  • A: haematogeneous metastasis without CNS involvement
    • single lesion
    • multiple lesions or

OR

  • B: CNS metastatic involvement
    1. pre-chiasmatic lesion
    2. CNS mass
    3. leptomeningeal disease
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