Presentation
History of progressive exertional dyspnea and episodes of cyanosis. Physical examination revealed a murmur. Electrocardiography demonstrated right bundle-branch block.
Patient Data
Age: 10 years
Gender: Female
From the case:
Ebstein anomaly
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There is marked cardiomegaly with a huge right atrial margin and somewhat squared or box-shaped appearance.
The aorta and main pulmonary artery segment are not well delineated.
The visualized pulmonary vascularity is within normal to slightly decreased.
From the case:
Ebstein anomaly
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Annotated image showing the box-shaped heart.
Author: Vincent Tatco
License: CC-NC-BY-SA
Case Discussion
This case shows the radiographic appearance of the cardiac silhouette in an echocardiographically proven Ebstein anomaly.
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