What is the clinical triad of tuberous sclerosis?
seizures, intellectual retardation, and adenoma sebaceum
What disease entity is considered a forme fustre of tuberous sclerosis?
There are multiple fat-attenuating lesions in the liver. Both kidneys are markedly enlarged and heterogeneous with multiple fat-attenuating parenchymal lesions. These lesions are compatible with hepatic and renal angiomyolipomas. Within the right kidney is a large predominantly hypoattenuating mass with a prominent and tortuous vessel traversing within it. This large hypodense lesion within the right kidney is well-defined except for its irregular posteromedial border.
The bowels are inferiorly displaced by the enlarged kidneys. Minimal ascites is seen.
There is an incidental finding of multiple cystic foci interspersed within the partially visualized bilateral lung parenchyma.
- CT (non-contrast):
- CT (C+ portal venous phase):
- CT (lung window):