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Usual interstitial pneumonia - scleroderma related

Case contributed by Bruno Di Muzio
Diagnosis probable

Presentation

Clinically established scleroderma. Shortness of breath.

Patient Data

Age: 75 years
Gender: Female

Diffuse reticular changes bilaterally are similar and compatible with fibrosis in the setting of scleroderma.

No superimposed consolidation is appreciated.

The cardiomediastinal contours are normal.

The bones are diffusely osteopaenic and there appears to be at least one mid-thoracic vertebral crush fracture.

Peripheral apicobasal interstitial involvement characterized by reticular opacities associated with micro and macro honeycombing foci and some traction bronchiectasis are seen. Ground-glass opacities are not a prominent feature in this study. Lung volumes are overall preserved. No evidence of esophageal dilation. 

Case Discussion

This case illustrates imaging follow-up in a patient with a known diagnosis of scleroderma and demonstrating scleroderma-related interstitial lung disease, which has a usual interstitial pneumonia (UIP) pattern. 

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