This is a case of histopathological proven infantile hepatic hemangioma, which is a neoplasm of liver caused by the proliferation of endothelial cells. It shows rapid growth in early stages and spontaneous involution.

The term “infantile hepatic hemangioma” is used instead of “hemangioendothelioma” because the clinicobiologic behavior is similar to infantile hemangiomas that occur elsewhere. It differs from adult epithelioid hemangioendothelioma in that it has malignant potential and does not involute.

It produces symptoms such as fetal cardiovascular compromise, hydrops fetalis, hepatomegaly, hemolytic anemia, thrombocytopenia, and unexplained congestive cardiac failure.

Therapeutic options include steroids, embolization, chemotherapy, radiotherapy, surgery, or liver transplantation.