Presentation
Patient with a report of bitemporal hemianopia and headache with onset 10 days ago.
Patient Data
Expansive formation with suprasellar epicenter, solid-cystic, presenting heterogeneous enhancement to the contrast medium, restriction of its solid component to diffusion and intermingling calcifications, with the cystic area being hyperintense on the T1-weighted sequence, inferring oily or protein content.
Case Discussion
Due to the neurological deficit characterized by visual loss and definition of a possible topography of neural involvement, magnetic resonance imaging was chosen, which showed a mass with a suprasellar epicenter and with characteristics of adamantinomatous craniopharyngioma, confirmed by an anatomopathological study of the specimen after surgical extraction.
Craniopharyngioma is a suprasellar tumor that mainly affects the pediatric age group, but it can also manifest in adults. It arises from remnants of Rathke's pouch and is considered a low-grade neoplasm that grows alongside very delicate neurovascular structures, such as the nerve optic, optic chiasm and carotid arteries.
It has two histological subtypes: papillary and adamantinomatous (now considered separate diagnoses in the 2021 5th edition of the WHO classification of CNS tumors.
The adamantinomatous is the most common and presents with solid-cystic components, whose cystic area is hyperintense on the T1-weighted magnetic resonance imaging sequence, translating protein or oily content, in addition to multiple hemorrhagic and calcium foci in the solid area.
The papillary subtype is less frequent and manifests as a summarily solid lesion.
Unable to process the form. Check for errors and try again.