Bilateral proximal radioulnar synostosis
At school, some difficulty is noticed when it comes to using the cutlery to eat and also to write. There was no pain or any other symptomatology. On examination, a limited supination was seen in both forearms, achieving maximum supination in an intermediate position, leaving the hands with the thumb up, causing pain when trying to supinate. Elbow flexion was normal and extension was limited by 10 °.
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Density and morphology of osseous structures are within usual limits. Bone fusion at the level of the proximal cubital and radial aspect bilaterally, in the configuration of proximal radioulnar synostosis.
Congenital radioulnar synostosis is a rare bone disorder that can occur isolated or associated with other disorders and that is characterized by a failure in the segmentation of the radius and ulna during embryonic development, limiting the movements of rotation of the forearm, which can lead to difficulties in some activities of daily life.
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- Dogra BB, Singh M, Malik A. Congenital proximal radioulnar synostosis. Indian J Plast Surg. 2003;36:36-8.