Patient Data
Severe plagiocephaly and copper beaten skull
Downward herniation of the cerebellar tonsils. There is also notable gyral impressions on the inner table and abnormal head shape.
Interval marked improvement in skull shape and size of the posterior fossa.
Case Discussion
This 6-month-old child has multiple sutural synostoses (sagittal suture and part of the lambdoid suture), and a Chiari I malformation.
Severe copper beaten skull appearance is present which is more reminiscent of a lacunar skull, however, no myelomeningocele is present (i.e not a Chiari II malformation) and axial imaging demonstrates the correlation of gyri with the overlying skull defects.
The patient was treated with surgery to open the sutures, and marked improvement to the skull shape and posterior fossa ensued.