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Chiari I malformation with syrinx

Case contributed by Mostafa Elfeky
Diagnosis almost certain

Presentation

Muscle weakness.

Patient Data

Age: 5 years
Gender: Female

MRI cervical spine

mri

There is cerebellar tonsils descent through foramen magnum compressing the cervicomedullary junction with resultant whole spinal cord syrinx. No associated hydrocephalic changes.

Annotated images

mri

The tonsillar herniation is estimated to be 7.2 mm below the foramen magnum (Chiari 1 malformation >6 mm).

Case Discussion

Child with a Chiari 1 malformation and resulting extensive syrinx involving the whole spinal cord (Holocord presentation).

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