Coat's disease

Case contributed by Dr Lana Rezan Pshtiwan

Presentation

Leukocoria of the left eye since birth.

Patient Data

Age: 2 months
Gender: Male
MRI

Left side vitreous body show abnormal signal; high signal on T1, low onT2 and intermediate on fat sat after contrast there is a thin linear After enhancement in the posterior 2/3. Atrophied  eft optic nerve.

Case Discussion

Coats' disease is telangiectatic retinal vessels with leakage of lipoproteinaceous exudate, while Persistent hyperplastic primary vitreous (PHPV) is usually associated with microphthlamoia and a persistent canal that goes from the optic nerve to the lens.

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