Craniofacial fibrous dysplasia

Case contributed by Dr Pavan Borra

Presentation

Right eye proptosis with right facial swelling

Patient Data

Age: 15 years
Gender: Male
CT

Expansion of frontal, sphenoid, ethmoid, maxillary bones as well as the mandibular ramus predominantly on right side with a ground glass matrix. There is encroachment of orbit and the sinuses on right side. Proptosis of right eye globe is noted.

Case Discussion

Fibrous dysplasia is benign developmental anamoly of mesenchymal precursor of bone with progressive replacement of normal bone marrow by immature fibrous-osseous tissue.

In craniofacial fibrous dysplasia  there is unilateral overgrowth of facial bones and calvarium with extended diploid space and outward expansion of outer table.

Differential diagnosis include; juvenile ossifying fibroma, cherubism , renal osteodystrophy.

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Case information

rID: 69395
Published: 9th Jul 2019
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

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