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Diffuse abdominal plexiform neurofibromatosis

Case contributed by Amr Farouk
Diagnosis almost certain

Presentation

Abdominal pain and increasing abdominal girth.

Patient Data

Age: 6 years
Gender: Female

Multiple solid fusiform masses along the distribution of nerves infiltrating throughout the hepatic hilum, small bowel mesentery and greater omentum. They are seen showing homogenous low attenuation.

Right femoral nerve thickening is noted as well.

Case Discussion

Pathologically proven diffuse abdominal and retroperitoneal plexiform neurofibromatosis.

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