Dysembryoplastic neuroepithelial tumor
1st episode of GTCS in a 20 year old female.
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A well demarcated cystic intracortical lesion in the left frontal lobe, following CSF in all sequence. The lesion has a soap bubble appearance with no surrounding edema. No enhancement noted on T1W images after administration of gadolinium. Few delicate septa like structures are visible within the lesion. No evidence of mass effect. There is evidence of scalloping of overlying frontal bone
Dysembryoplastic neuroepithelial tumors are benign tumor (WHO grade 1). DNET are one of most common cause for seizures in children.
DNET are supratentorial and characterized by intracortical location, multinodular architecture, and heterogeneity in cellular composition 1,2.
Differentials to be considered:
- ganglioglioma: contrast enhancement present with calcification
- pleomorphic xanthoastrocytoma: contrast enhancement with dural tail sign
- 1. Daumas-Duport C, Scheithauer BW, Chodkiewicz JP et-al. Dysembryoplastic neuroepithelial tumor: a surgically curable tumor of young patients with intractable partial seizures. Report of thirty-nine cases. Neurosurgery. 1989;23 (5): 545-56. Pubmed citation
- 2. Stanescu Cosson R, Varlet P, Beuvon F et-al. Dysembryoplastic neuroepithelial tumors: CT, MR findings and imaging follow-up: a study of 53 cases. J Neuroradiol. 2002;28 (4): 230-40. Pubmed citation