Presentation
Facial deformity in a teenager.
Patient Data
Age: 16
Gender: Male
From the case:
Fibrous dysplasia of the orbital roof
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Axial CT images of the skull (bone window) revealed an expansile bone lesion with a typical ground glass appearance involving the roof of the right orbit.
Note the mass effect on the ipsilateral frontal sinus and right orbit.
Case Discussion
Fibrous dysplasia is a developmental anomaly manifested as a defect in osteoblastic differentiation and maturation. It can affect any bone of the body. The skull and facial bones are the affected sites in 10–25% of patients with monostotic fibrous dysplasia and in 50% of patients with polyostotic fibrous dysplasia.
CT radiological features have three patterns:
- Ground glass pattern (>50%): as in this case.
- Homogeneously dense pattern (~25%).
- Cystic pattern (~20%).
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