Intraosseous haemophilic pseudotumor

Case contributed by Prashant Mudgal
Diagnosis probable

Presentation

Known case of hemophilia presented with pain and swelling in right knee

Patient Data

Age: 30 years
Gender: Male

There is a well-defined, slightly expansile, osteolytic lesion seen involving proximal right tibia. The lesion is surrounded by a thin sclerotic rim and displaying thin incomplete septa-like structures.

Lateral radiograph shows scalloping of the posterior margin of tibia (smaller arrows in the annotated image) and radiating trabeculae (larger arrow in the annotated image) mimicking a malignant or infectious periosteal reaction.

In a known case of hemophilia and considering the age of the patient, imaging features are most likely suggestive of an intraosseous haemophilic pseudotumor.

Case Discussion

Hemophilic pseudotumor is a rare complication occurring in 1–2% of patients with severe hemophilia.

Image differentials include:

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.