Langerhans cell histiocytosis

Case contributed by Dr Ruslan Asadov

Patient Data

Age: 20 years
Gender: Male
CT

see below

Case Discussion

Langerhans cell histiocytosis. Hand Schueller Christian: Chronic disseminated form, multifocal.

20 year old boy with diabetes insipidus, cough, fever, shortness of breath.

Conventional  CT reveals multiple small nodules thin-walled, irregular cysts predominantly in the upper 1/3 of the lungs.

Lytic defect of the parietal, frontal and maxillary bones in the skull.

Other lytic lesions in the femur (no image)

Etiology: Uncertain; Inflammatory ~ neoplastic

Epidemiology:  Affects 4 per 1 million                                                             

 Gender: M:F = 2:1

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Case information

rID: 7536
Published: 7th Nov 2009
Last edited: 20th May 2019
Inclusion in quiz mode: Included

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