Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) - ectopic fused kidneys
Presentation
Had surgery for renal anomalies 10 years ago.
Patient Data
Both kidneys are fused, malrotated, and in an ectopic position in the right pelvis, with dilatation of the renal pelvis and calyces. The two renal pelves seem to communicate with each other, forming a single renal pelvis with an anastomosis at the anterosuperior angle of the urinary bladder (visualized on sagittal T2 sequences). No visualization of the ureters.
No visualization of the uterus and vagina with normal appearances of the ovaries, containing small follicles.
Case Discussion
MRI features of Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with ectopic fused kidneys (type B).
We do not have the report of the previous surgery but it seems that the patient had a pyelovesical anastomosis most likely for associated ureteric anomalies.
Additional contributor: A. Ramdani, MD
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