Polysplenia syndrome

Case contributed by Dr Ian Bickle


This 55 year old female attended respiratory clinic with a persistent cough. The resulting chest radiograph prompted further investigation with CT.

Patient Data

Age: 55 years
Gender: Female

In summary:

Case Discussion

Features of polysplenia syndrome (a.k.a. left sidedness or left isomerism):

  • interruption of the hepatic segment of the IVC with azygos continuation (present in 65% of cases); the azygos vein is typically also enlarged
  • multiple spleens - usually at least one almost normal sized spleen with numerous additional spleens of variable size
  • dextrocardia is present in 35-40% of cases with the prevalence of congenital heart disease even higher at nearly 1 in 2 patients
  • hepatic veins drain directly into the right atrium
PlayAdd to Share

Case information

rID: 18841
Published: 24th Jul 2012
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.