Presentation
Known case of aortic valve regurgitation with progressive shortness of breath.
Patient Data
The aortic valve exhibits four equal-sized cusps (one right coronary cusp, one left coronary cusp and two non-coronary cusps) and calcifications.
Calcifications are also seen along the aorta and coronary arteries reflective of atherosclerotic disease.
There is cardiomegaly with dilated left ventricle.
Case Discussion
This case demonstrates a patient with quadricuspid aortic valve (QAV), which is a rare congenital valvular anomaly wherein there are four cusps, instead of the usual three, in the aortic valve. In this case, the aortic valve is composed of four equal-sized cusps (type a QAV). The most common complication of this valvular anomaly is aortic regurgitation due to inadequate closing of the four cusps during systole.