Scleroderma with interstitial fibrosis

Case contributed by Dr Natalie Yang

Presentation

Shortness of breath.

Patient Data

Age: Adult
Gender: Female

HRCT of the chest demonstrates characteristic changes of pulmonary fibrosis, particularly in the bases and in the subpleural lung. Honeycomb change, intralobular septal thickening and traction bronchiectasis are all present. No pleural effusion or obvious nodal enlargement is visible.

The esophagus is dilated and air filled.

Case Discussion

The combination of basal pulmonary fibrosis and a dilated esophagus, is certainly suggestive of scleroderma.  Although not pathognomonic it should be considered highly likely, especially in a woman. 

In this case, the patient had clinically established scleroderma.

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Case information

rID: 8604
Published: 16th Feb 2010
Last edited: 16th Jul 2018
System: Chest
Inclusion in quiz mode: Included

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