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Situs ambiguous - polysplenia syndrome type

Case contributed by Mohammad Taghi Niknejad
Diagnosis probable

Presentation

Heart murmur at physical exam

Patient Data

Age: 4 years
Gender: Male

The cardiac apex is on the right. Transverse liver is noted with stomach on the right and also multiple spleens on the right with interruption of intrahepatic IVC with azygous continuation of IVC.

Case Discussion

The findings are consistent with situs ambiguous (also called heterotaxy) - polysplenia syndrome type. 

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