Usual interstitial pneumonia pattern: idiopathic pulmonary fibrosis
Discussion:
This case provides us with the typical UIP pattern of interstitial lung disease. The differential diagnosis of this pattern is not limited to IPF but also includes other conditions such as:
- mixed connective tissue and collagen vascular disorders with IPF
- asbestosis
- chronic hypersensitivity pneumonitis
- chronic pulmonary drug toxicity
- recurrent aspiration
- fibrosing NSIP
The presence of distal esophageal dilatation raises the possibility of mixed connective tissue disease/scleroderma associated with IPF.
The presence of hiatus hernia raise the possibility of repeated microaspiration as an etiological factor.
Open lung biopsy showed idiopathic pulmonary fibrosis (IPF).
Related articles:
- Asbestosis
- Aspiration
- Chronic aspiration pneumonia
- Chronic hypersensitivity pneumonitis (historical)
- Connective tissue disease
- Fibrotic non-specific interstitial pneumonitis
- Hiatus hernia
- Idiopathic pulmonary fibrosis
- Interstitial lung disease
- Mixed connective tissue disease
- Scleroderma (pulmonary manifestations)
- Usual interstitial pneumonia
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