Benign external hydrocephalus or Benign enlargement of the subarachnoid spaces (BESS) is typically
characterized clinically by macrocrania and frontal bossing.
BESS is more common in males
and there is often a family history of macrocrania.
It is theorized to be due to a
delay in development of arachnoid villi in the saggital sinus leading to faulty
CSF resorption.
Imaging features include:
- widening
of bifrontal CSF spaces > 5mm
- no
flattening of adjacent gyri
- enlarged
anterior fontanelle
- normal
ventricle size and no atrophy
- no
blood products
- no
cortical vein displacement
The enlarged subarachnoid fluid collection usually
resolves by age 2, however, the macrocrania may persist.
While BESS is typically benign, there have been
reported associations with increased risk of subdural hemorrhage, communicating
hydrocephalus, and psychomotor delay.