Diagnosis: Dysplastic cerebellar gangliocytoma (Lhermitte-Duclos disease) by MRI features.

Differential diagnosis of this case includes:

• cerebellar infarction: excluded by DWI
• acute cerebellitis: excluded by clinical picture
• rhombencephalosynapsis: excluded as cerebellar vermis is present

The patient was referred for upper and lower GI endoscopy searching for polyps as this condition is associated with Cowden syndrome.