What percentage of angiomyolipomas are associated with TS (tuberous sclerosis)?
Only 20% of angiomyolipomas are associated with tuberous sclerosis.
How do angiomyolipomas in tuberous sclerosis differ from those that are sporadic?
They are usually very numerous (like this case), and bilateral.
What imaging investigation would confirm the diagnosis of tuberous sclerosis in this patient? What findings would you expect to find?
CT of the brain (or MRI) will in the vast majority of cases show typical features (subependymal nodules, cortical/ subcortical hamartomas).
Both kidneys contain innumerable predominantly fat density nodules consistent with angiomyolipomas.