There is a dysplastic appearance of the cochlea, which is much smaller than expected. Only a basal turn is distinctly identified. There is no appreciable interscapular septae and modiolus. The vestibule is dilated. There is a dysplastic appearance of the lateral semicircular canal, noting that the lateral semicircular canal. There is stenosis of the cochlear aperture. The ossicular chain is intact with the stapes footplate in the oval window.