What are the three main differentials for single hemispheric atrophy?
Dyke-Davidoff-Masson Syndrome, Rasmussen Encephalitis, Sturge-Weber Syndrome
How can you differentiate between Rasmussen encephalitis, Dyke-Davidoff-Masson Syndrome and Sturge-Weber Syndrome?
Dyke-Davidoff-Masson = compensatory calvarial changes Sturge-Weber = pial angiomata with enhancement, cortical calcifications Rasmussen = neither!
Patient age 14 years old. Left superior temporal gyrus resection, minimal surrounding gliosis. Left mesial temporal lobe was relatively spared with symmetrical hippocampi, ventricles and caudate nuclei.