Presentation
Bilateral sensorineural hearing loss
Patient Data
Age: 4 years
Gender: Female
From the case:
Cochlear incomplete partition type II
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bilateral coalescence of the apical and middle turns of both cochleae giving cystic appearance of the cochlear apex
dysplastic right lateral semicircular canal confluent with cystic vestibule
mildly dilated left vestibular aqueduct
From the case:
Cochlear incomplete partition type II
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MRI confirms the findings of CT in the form of:
bilateral 1.5 turns of the cochleae with cystic cochlear apex. The basal turns are well developed
mildly dilated left endolymphatic sac
Case Discussion
Findings are consistent with bilateral cochlear incomplete partition type II.