This is a case of complex congenital heart disease with Dextrocardia, DORV, VSD, persistent left SVC & partial anomalous pulmonary venous return (PAPVR).
Double outlet right ventricle (DORV) is a rare congenital cardiac anomaly where the aorta and the pulmonary artery arise from the right ventricle. VSD is invariably present.
The morhological right ventricle criteria are:
- Triangular configuration.
- Moderator band at its apex.
- Coarse trabecular pattern at its apical septum.
- Muscular band around its out ventricular tract with the its atrioventricular and ventriculo-arterial valves separated by muscle.
The septal surface of the morphological left ventricle is smooth.
The left atrial appendage is finger-like while the right atrial appendage is triangular.