Dextrocardia, DORV, VSD, persistent left SVC & PAPVR

Discussion:

This is a case of complex congenital heart disease with Dextrocardia, DORV, VSD, persistent left SVC & partial anomalous pulmonary venous return (PAPVR).

Double outlet right ventricle (DORV) is a rare congenital cardiac anomaly where the aorta and the pulmonary artery arise from the right ventricle. VSD is invariably present. 

The morhological right ventricle criteria are:

  • Triangular configuration.
  •  Moderator band at its apex. 
  • Coarse trabecular pattern at its apical septum.
  • Muscular band around its out ventricular tract with the its atrioventricular and ventriculo-arterial valves separated by muscle.

The septal surface of the morphological left ventricle is smooth.

The left atrial appendage is finger-like while the right atrial appendage is triangular. 

 

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