Isolated absence of the right pulmonary artery
Additional information garnered from patient's file reinforces diagnosis of IUAPA:
- hypoplastic right lung with severely decreased ventilation and no perfusion, discovered incidentally on a V/Q scan performed at toddlerhood due to suspicion of foreign body aspiration
- findings at report for chest CT performed at age 5 very similar to above exam
- transthoracic echocardiography at age 8 demonstrated no cardiac anomaly
- patient's mother mentions mediastinal shift to right on chest x-ray taken at age 4 months
Differential diagnosis of a small lung on plain film includes:
- hypogenetic lung syndrome (scimitar syndrome)
- (isolated) unilateral pulmonary artery interruption/atresia/absence
- Swyer-James-MacLeod syndrome
- post-lobectomy
{"caseId":52180,"playlists":[],"playlist_ids_include_case":[]}