A Mondini malformation is an inner ear abnormality that consists a triad :

1. abnormal cochlea
   • only 1.5 turns (instead of the normal 2.5 turns)
   • normal basal turn with a cystic apex in place of the distal 1.5 turns
2. enlarged vestibule with normal semicircular canals
3. enlarged vestibular aqueduct containing a dilated endolymphatic sac

A case of Dr. Masood Gholamian, Tabriz university.