The above described findings are consistent with Dyke-Davidoff-Masson syndrome (hemispheric infarction) with left cerebral hemiatrophy and fronto-parietal encephalomalacia, likely due to in-utero vascular insult.

The differential diagnosis includes:

Chronic Rasmussen encephalitis (chronic, progressive, unilateral inflammation of brain of uncertain etiology with hemispheric volume loss and intractable focal seizure activity ) however, Rasmussen encephalitis tends not to have calvarial changes.

Sturge-Weber syndrome

• • • progressive hemispheric atrophy and enhancement of pial angiomas
    • cortical calcifications
    • port-wine facial nevus (clinically)