Here is a case of a unicornuate uterus (type a1b) associated with dorsal pancreatic agenesis. Association between Mullerian duct anomalies and dorsal agenesis of the pancreas is uncommon as genitourinary organs and pancreas have a separate embryologic origin ¹.

A unicornuate uterus is a type of class II Mullerian duct anomaly. It is subclassified according to the American Fertility Society as follows:

• type a: with rudimentary horn 

  • a1: horn contains endometrium

    • a1a: communicating contralateral rudimentary horn contains endometrium (10%)

    • a1b: non-communicating contralateral rudimentary horn contains endometrium (22%)

  • a2: contralateral horn has no endometrial cavity (33%)

• type b: no horn (35%)